Human COQ3 (Ubiquinone biosynthesis O-methyltransferase, mitochondrial) ELISA KIT (HUFI05160)

COQ3 catalyzes critical O-methylation steps during the biosynthesis of coenzyme Q10 (ubiquinone) within the mitochondrial matrix, and altered expression of this enzyme is increasingly linked to primary coenzyme Q10 deficiency, mitochondrial myopathies, and neurodegenerative phenotypes. The microplate-based immunoassay from Assay Genie allows researchers to quantify COQ3 protein levels in human blood-derived samples, with antibody reactivity validated specifically for human COQ3 (no significant cross-reactivity with mouse or rat), supporting translational work on oxidative phosphorylation, respiratory chain function, and cellular metabolic models. Each kit contains reagents sufficient for 96 individual determinations and is intended for in vitro research use only; refrigerated storage preserves antibody activity. Typical applications include biomarker profiling in patient cohorts, pathway analysis in mitochondrial disease models, and pharmacodynamic studies exploring the regulation of ubiquinone production under oxidative stress conditions.